Abstract

LVNC is a rare cardiomyopathy characterized by abnormal trabeculae in the left ventricle that form a sponge-like myocardium, leading to contractile dysfunction and poor filling. In addition to this characteristic, the condition may or may not be associated with another structural cardiac abnormality. This case demonstrates how the ratio of the myocardium’s compaction component to a noncompacted component can lead to the diagnosis of LV NC. However, with nutrition and oxygenation, the regrowth in a neonate showed improvement. Prenatal diagnosis of LVNC is problematic for various reasons since findings can overlap with those of normal physiologic variants or other conditions such as dilated cardiomyopathy and hypertrophic cardiomyopathy. To address this, echocardiography assessing the NC: C ratio has shown to be effective, with a value ≥2 being diagnostic for LVNC.